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Case report
A novel approach to the treatment of a direct carotid–cavernous fistula in a patient with Ehlers–Danlos syndrome type IV
  1. Ichiro Nakagawa1,
  2. Hun Soo Park1,
  3. Takeshi Wada2,
  4. Katsutoshi Takayama2,
  5. Hiroyuki Nakagawa2,
  6. Kimihiko Kichikawa2,
  7. Hiroyuki Nakase1
  1. 1Department of Neurosurgery, Nara Medical University, Kashihara, Nara, Japan
  2. 2Department of Radiology, Nara Medical University, Kashihara, Japan
  1. Correspondence to Dr I Nakagawa, Department of Neurosurgery, Nara Medical University, Kashihara, Nara 634-8522, Japan; nakagawa{at}naramed-u.ac.jp

Abstract

We report a case of a direct carotid–cavernous fistula (CCF) in a patient with Ehlers–Danlos syndrome type IV who presented with progressive chemosis and diplopia. To prevent potential lethal arterial wall injury due to the fragility of the arterial vessel wall, the ipsilateral carotid artery and internal jugular vein were surgically exposed for direct insertion of endovascular sheaths, and transvenous embolization was performed using triple microcatheters with detachable coils. The clinical course was uneventful, and chemosis and diplopia subsequently resolved. By the 6 month follow-up, MRI revealed no recurrence of the CCF. These techniques offer a unique access alternative for endovascular treatment, thereby reducing the risks associated with arterial dissection that often accompanies transfemoral access in this particular condition.

  • Fistula
  • Intervention
  • Vessel Wall

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