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CASE REPORT
Cerebral vascular findings in PAPA syndrome: cerebral arterial vasculopathy or vasculitis and a posterior cerebral artery dissecting aneurysm
  1. Kasra Khatibi1,
  2. Jeremy J Heit2,
  3. Nicholas A Telischak2,
  4. Jorina M Elbers3,
  5. Huy M Do4
  1. 1Department of Neurology, Stanford University, Stanford, California, USA
  2. 2Department of Radiology, Stanford University, Stanford, California, USA
  3. 3Department of Neurology, Stanford University, Stanford, California, USA
  4. 4Departments of Radiology and Neurosurgery, Stanford University, Stanford, California, USA
  1. Correspondence to Dr Kasra Khatibi, Department of Neurology, Stanford University, 300 Pasteur Drive h3142, Palo Alto, CA 94304, USA; kkhatibi{at}stanford.edu

Abstract

A young patient with PAPA (pyogenic arthritis, pyoderma gangrenosum, and acne) syndrome developed an unusual cerebral arterial vasculopathy/vasculitis (CAV) that resulted in subarachnoid hemorrhage from a ruptured dissecting posterior cerebral artery (PCA) aneurysm. This aneurysm was successfully treated by endovascular coil sacrifice of the affected segment of the PCA. The patient made an excellent recovery with no significant residual neurologic deficit.

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